Reference

Gender, age

Segmental lesions

Since birth or in childhood

Acquired lesions later on

Family history

Berger & Hundeiker [10]

M, 22 y

Plaque on left buttock

?

Right knee, right thoracal area

Brother and sister with disseminated lesions

Naversen et al. [12]

F, 12 y

Plaque on right arm

Since early childhood

Right buttock

Maternal great-grandfather and great-aunt with disseminated lesions

Landthaler et al. [13] case 1

M, 1 month

Plaque on back

Since birth

Face and neck

No

Tomasini et al. [14]

F, 45 y

Plaque on left abdomen

Since birth

Trunk and extremities

Two sisters with disseminated lesions

Glick et al. [15]

F, 9 y

Plaque on left abdomen

Since birth

Back and upper arms

No

Hamlet et al. [16]

M, 17 y

Linear band on right flank

Since childhood (age 7 y)

Arms and upper thorax

No

Flórez et al. [17]  case 1

F, 22 y

Patch on left arm and right ankle

Since birth

Right buttock and thigh

Father, paternal grandfather and paternal cousin with “similar lesions”

“ “ case 2

F, 72 y

Plaque on right wrist

Since birth

Left arm, breast and leg

No

“ “ case 3

F, 82 y

Plaque on left elbow

Since birth

Right hand and forearm

No

Peña-Penabad et al. [18] case 2

F, 61 y

Plaque on left thigh

Since birth

Right buttock and arm

Granddaughter of the patients’ brother had (type 1)  segmental lesions

Allombert-Blaise et al. [19]

F, 9 y

Plaques on right clavicular area, left thorax and abdomen

Since birth

Both arms and left leg

No

Our case

M, 39 y

Linear band on right thorax

Since early childhood

Left wrist and both thighs

No